Macrophage activation syndrome in Kawasaki disease.
نویسندگان
چکیده
BACKGROUND Kawasaki disease is an acute febrile vasculitis of childhood. Macrophage activation syndrome is a rare life threatening complication. CASE CHARACTERISTICS 4-year-old boy with Kawasaki Disease treated with intravenous immunoglobulins. OBSERVATION He developed encephalopathy, hepatosplenomegaly and pancytopenia. Blood investigations and bone marrow aspiration suggested macrophage activation syndrome. OUTCOME Good response to pulse methylprednisolone (30 mg/kg/d) for 5 days. MESSAGE Macrophage activation syndrome may complicate Kawasaki disease.
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ورودعنوان ژورنال:
- Indian pediatrics
دوره 51 2 شماره
صفحات -
تاریخ انتشار 2014